Yeni Doğanda Görülen Lignöz Konjoktivit ve Dandy-Walker Spektrumu İlişkisi:Nadir Bir Olgu Ligneous Conjunctivitis in a Dandy-Walker Spectrum:A Rare Case
نویسندگان
چکیده
Lignöz konjoktivit, genellikle tip 1 plazminojen eksikliği
 ile karakterize bir hastalıktır. Genetik kalıtımlı
 olduğu gibi enfeksiyon veya travma de ilişkili
 olabilir. Özellikle tarsal konjonktivada görülen odunsu
 görünümde fibrinden zengin psödomembranlarla
 karakterizedir. Tedavisinde; heparin, alfa kimotripsin,
 topikal hiyalüronidaz, kortikosteroidler, siklosporin ve
 membranların cerrahi eksizyonu yer almaktadır. Bu
 çalışmada, hidrosefali nedeniyle ventrikülo-peritoneal
 şant uygulanmış 10 aylık erkek hastada Dandy-
 Walker spektrumuna bağlı ve lignöz
 konjonktivit birlikteliğini göstermek amaçlanmıştır.
منابع مشابه
Dandy-Walker Syndrome
Epidemiology Incidence is approximately 1 in 25-35,000 live births. [3] It occurs slightly more frequently in females than in males. Marked variation has been shown in the genetics and aetiology. Most cases of DWS are sporadic, although familial occurence has been reported and several individuals with de novo interstitial deletions of 3q have been identified. [4] DWS may result from chromosomal...
متن کاملDandy-Walker Syndrome
Epidemiology Incidence is approximately 1 in 25-35,000 live births. [3] It occurs slightly more frequently in females than in males. Marked variation has been shown in the genetics and aetiology. Most cases of DWS are sporadic, although familial occurence has been reported and several individuals with de novo interstitial deletions of 3q have been identified. [4] DWS may result from chromosomal...
متن کاملDandy-Walker Malformation
Dandy-Walker malformation is a rare congenital malformation and involves the cerebellum and fourth ventricle. The condition is characterized by agenesis or hypoplasia of the cerebellar vermis, cystic dilatation of the fourth ventricle, and enlargement of the posterior fossa. A large number of concomitant problems may be present, but the syndrome exists whenever these three features are found. A...
متن کاملDandy-Walker Syndrome
Dandy-Walker Syndrome is a congenital brain defect in humans [4] characterized by malformations to the cerebellum [5], the part of the brain that controls movement, and to the ventricles, the fluid-filled cavities that surround the cerebellum [5]. The syndrome is named after physicians Walter Dandy and Arthur Walker, who described associated signs and symptoms of the syndrome in the 1900s. The ...
متن کاملAsymptomatic Dandy-Walker syndrome in an adult
This 34 years old man presented with moderate and persistent headache occurring 48 hours following Benin head injury. There were no symptoms of increased intracranial pressure. Neurological examination was unremarkable without cerebellar ataxia or psychomotor retardation .the patient was submitted to CT scan and magnetic resonance imaging (MRI) of the brain that revealed agenesis of cerebellar ...
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ژورنال
عنوان ژورنال: Süleyman Demirel Üniversitesi T?p Fakültesi dergisi
سال: 2021
ISSN: ['1300-7416', '2602-2109']
DOI: https://doi.org/10.17343/sdutfd.806926